Systemic Sclerosis with Multiple
Pulmonary Manifestations
Published: June 1, 2016 | DOI: https://doi.org/10.7860/JCDR/2016/.8032
Mohan Rao Kotnur, Parinita Suresh, Venkata Siva Prasad Reddy, Tarun Sharma, Nabil Ahmed Salim
1. Professor and Head, Department of Respiratory Medicine, Rajarajeswari Medical College and Hospital, Bangalore, India.
2. Post Graduate Student, Department of Respiratory Medicine, Rajarajeswari Medical College and Hospital, Bangalore, India.
3. Post Graduate Student, Department of Respiratory Medicine, Rajarajeswari Medical College and Hospital, Bangalore, India.
4. Post Graduate Student, Department of Respiratory Medicine, Rajarajeswari Medical College and Hospital, Bangalore, India.
5. Post Graduate Student, Department of Respiratory Medicine, Rajarajeswari Medical College and Hospital, Bangalore, India.
Correspondence
Dr. Mohan Rao Kotnur,
Professor and Head, Department of Respiratory Medicine, Rajarajeswari Medical College and Hospital,
Mysore Road, Kengeri Hobli, Bangalore-74, India.
E-mail: kotnur.rao@gmail.com
Systemic sclerosis (SSc) is a chronic autoimmune multisystem disorder characterized by endothelial dysfunction and fibroblast dysfunction, which results in progressive fibrosis of the skin and internal organs more frequently the lungs and gastro intestinal tract. Pulmonary involvement is common in the course of SSc, with Interstitial Lung Disease (ILD) and Pulmonary Arterial Hypertension (PAH) being the leading causes of death. Here we report, case of an elderly female patient presenting with Diffuse SSc with multiple uncommon pulmonary manifestations like ILD with Usual Interstitial Pneumonia (UIP) pattern (usually less common), PAH and right sided pleural effusion.
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